Lung tumors
(Lungentumore im Kindes- und Jugendalter)

  • Metastases (Wilms tumor, neuroblastoma, ...).
  • Pleuropulmonary blastoma (PPB): rare and highly aggressive malignant tumor of the lung. 25% are extrapulmonary. Metastases are usually found in the central nervous system. The tumor may be associated with CCAM.
    - The tumor arises from the lung or the pleura or both sites.
    - There seems to be a constitutional and heritable predisposition to other dysplastic and neoplastic diseases (cystic nephroma, pulmonary cysts) in 25% of these patients. The families should be investigated carefully.
    - Bilateral PPB has been described.
    - Poor prognosis.
  • Embryonal rhabdomyosarcoma is also very rare. 35% arise from pre-existing pulmonary cystic malformations (CCAM).
  • Bronchial carcinoid.
  • Bronchial mucoepidermoid tumors.
  • Inflammatory pseudo-tumor (synonyms: plasma cell granuloma, histiocytoma, fibrous xanthoma).
    - Suspected aetiology: uncontrolled reaction to tissue damage or chronic inflammation.
    - 50% of patients under the age of 16.
    - 40% without any symptoms.
    - Symptoms: cough, fever, wheezing, fatigue, lower respiratory tract infection.
    - Histologically: spindle cells, myofibroblasts, granulomatous inflammation, lymphoid hyperplasia, fibrosis.
    - Invasive growth (vascular invasion, bone destruction) recurrence and metastases can occur.
    - Needle biopsy may lead to an unclear diagnosis. Surgery is mandatory.
Inflammatory pseudo-tumor surrounding the main bronchus
Inflammatory pseudo-tumor surrounding the main bronchus
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